PubTransformer

A site to transform Pubmed publications into these bibliographic reference formats: ADS, BibTeX, EndNote, ISI used by the Web of Knowledge, RIS, MEDLINE, Microsoft's Word 2007 XML.

Misdiagnosed anomalous left coronary artery from the pulmonary artery as endocardial fibroelastosis in infancy: A case series.

Abstract Anomalous left coronary artery from the pulmonary artery (ALCAPA) is a rare but severe congenital cardiac malformation. The prognosis mainly depends on the early and accurate diagnosis and treatment. However, without a typical and specific clinical manifestation in early stage, ALCAPA has a higher rate of false initial diagnosis.
PMID
Related Publications

Resolution of pathologic Q wave, left ventricular dysfunction and mitral regurgitation after dual coronary repair of the anomalous origin of the left coronary artery from the pulmonary artery.

Diagnosis and surgery of anomalous origin of the left coronary artery from the pulmonary artery in children.

Anomalous origin of the left coronary artery from the pulmonary artery in children: 15 years experience.

Anomalous origin of the left coronary artery from the pulmonary artery in infants: clinical features and the perioperative treatment strategies.

Two congenital coronary abnormalities affecting heart function: anomalous origin of the left coronary artery from the pulmonary artery and congenital left main coronary artery atresia.

Authors

Mayor MeshTerms
Keywords
Journal Title medicine
Publication Year Start




PMID- 28614263
OWN - NLM
STAT- In-Process
DA  - 20170614
LR  - 20170614
IS  - 1536-5964 (Electronic)
IS  - 0025-7974 (Linking)
VI  - 96
IP  - 24
DP  - 2017 Jun
TI  - Misdiagnosed anomalous left coronary artery from the pulmonary artery as
      endocardial fibroelastosis in infancy: A case series.
PG  - e7199
LID - 10.1097/MD.0000000000007199 [doi]
AB  - INTRODUCTION: Anomalous left coronary artery from the pulmonary artery (ALCAPA)
      is a rare but severe congenital cardiac malformation. The prognosis mainly
      depends on the early and accurate diagnosis and treatment. However, without a
      typical and specific clinical manifestation in early stage, ALCAPA has a higher
      rate of false initial diagnosis. DIAGNOSTIC AND THERAPEUTIC PROCEDURE: Three
      infants with impaired left ventricle (LV) function, LV enlargement, mitral valve 
      regurgitation (MR), and LV endocardium thickness were initially diagnosed as
      endocardial fibroelastosis (EFE). Due to the treatment effectiveness with
      prednisone acetate and digoxin, abnormal Q waves with T inversion, and dilated
      right coronary artery (RCA), the diagnosis of ALCAPA was suspected. Lastly,
      cardiac angiography confirmed the diagnosis. All of them were transferred to the 
      cardiac surgery department and received a successful surgical repair. The
      follow-up results showed that abnormal Q waves with T waves inversion on
      electrocardiogram gradually regressed and disappeared, LV ejection fraction and
      LV dilation returned to a normal range after surgery, with alleviation of MR.
      Besides, endocardial thickness secondary to ischemia also returned to normal.
      CONCLUSION: ALCAPA should be suspected when confronted with patients with left
      heart enlargement, impaired left ventricular function, and signs of myocardial
      ischemia, particularly in infancy. EFE is an important differential diagnosis and
      may also arise as a result of ALCAPA. Abnormal Q waves with T waves inversion,
      particularly in avL, dilated RCA and increased ratio of RCA/AO are important
      differential key points for the identification of ALCAPA and EFE. Awareness of
      this condition is essential for prompt recognition and referral to a tertiary
      cardiac center to enable early surgical intervention and improved prognosis for
      these children.
FAU - Ma, Fan
AU  - Ma F
AD  - aDepartment of Pediatric, West China Second University Hospital, Sichuan
      University bWest China Medical School of Sichuan University cThe Cardiac
      Development and Early Intervention Unit, West China Institute of Women and
      Children's Health, West China Second University Hospital, Sichuan University dKey
      Laboratory of Birth Defects and Related Diseases of Women and Children (Sichuan
      University), Ministry of Education, Chengdu, Sichuan, China.
FAU - Zhou, Kaiyu
AU  - Zhou K
FAU - Shi, Xiaoqing
AU  - Shi X
FAU - Wang, Xiaoqing
AU  - Wang X
FAU - Zhang, Yi
AU  - Zhang Y
FAU - Li, Yifei
AU  - Li Y
FAU - Hua, Yimin
AU  - Hua Y
FAU - Wang, Chuan
AU  - Wang C
LA  - eng
PT  - Journal Article
PL  - United States
TA  - Medicine (Baltimore)
JT  - Medicine
JID - 2985248R
EDAT- 2017/06/15 06:00
MHDA- 2017/06/15 06:00
CRDT- 2017/06/15 06:00
AID - 10.1097/MD.0000000000007199 [doi]
AID - 00005792-201706160-00049 [pii]
PST - ppublish
SO  - Medicine (Baltimore). 2017 Jun;96(24):e7199. doi: 10.1097/MD.0000000000007199.

<?xml version="1.0" encoding="UTF-8"?>
<b:Sources SelectedStyle="" xmlns:b="http://schemas.openxmlformats.org/officeDocument/2006/bibliography"  xmlns="http://schemas.openxmlformats.org/officeDocument/2006/bibliography" >
</b:Sources>